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Myectomy-myotomy for long segment Hirschsprung's disease in a patient with Haddad syndrome

, : Myectomy-myotomy for long segment Hirschsprung's disease in a patient with Haddad syndrome. Journal of Pediatric Surgery 44(3): 620-622

Hirschsprung's disease is a rare entity with an incidence of 1 in 5000 live born infants. Long segment Hirschsprung's disease occurs in approximately 5% to 10% of this patient population and is defined as a transition zone proximal to the sigmoid colon (Bodian M, Carter CO, Ward BC. Hirschsprung's disease. Lancet. 1951;1:302-309). The association of congenital central hypoventilation syndrome (also known as Ondine's curse) and Hirschsprung's disease is termed Haddad syndrome.


PMID: 19302869

DOI: 10.1016/j.jpedsurg.2008.10.115

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